问题 问答题 简答题

试述遗传性代谢缺陷病的病理生理特点。

答案

参考答案:

遗传性代谢缺陷病的病理生理改变可分为3类:①通过该代谢途径的某些终末产物缺乏,如过氧化酶体病溶酶体病等,症状多为持续性、进行性,且与进食等因素无关。②受累代谢途径的中间和(或)旁路代谢产物大量蓄积,如苯病酮尿症、半乳糖血症等;发病或早或迟,发病前常有无症状期,或症状呈间隙发作。③由于代谢途径受阻而导致对肝、脑、肌等组织供能不足,如糖代谢障碍、先天性高乳酸血症等,临床表现为低血糖、高乳酸血症等。

填空题
阅读理解

Chinese politeness have always been formal to follow strict rules, although sometimes Chinese people seem to be impolite according to Western standards in public places. To well understand Chinese, some concepts should not be ignored.

Mianzi

The idea of shame, usually expressed as 'face' could be loosely defined as the 'status' or 'self-respect' in Chinese and by no means alien to foreigners. It is the worst thing for a Chinese to lose face. Never insult, embarrass, shame, yell at or otherwise demean a person. Since all these actions would risk putting a Chinese in a situation that he might lose face, neither try to prove someone wrong nor shout at him in public. In order to get a successful effect without letting a Chinese lose face, any criticism should be delivered privately, carefully, or else, just opposite to what you wish.

Guanxi

Throughout much of Chinese history, the fundamental glue that has held society together is the concept of guanxi, relationships between people. It is very important for the Chinese to have good relationships. They often regard good social relations as a symbol of personal ability and influence. Someone who has no connections would be disrespected and is only half-Chinese.

Keqi

Keqi not only means considerate, polite, and well mannered, but also represents respect and modesty. It is impolite to talk too proudly about oneself or one's inner circle. The expression is most often used in the negative, as in buyao keqi, meaning "you shouldn't be so kind and polite to me," or "you're welcome."

Besides, Chinese seldom express what they think directly and they prefer a roundabout way. Neither show their emotions and feelings in public. They rarely greet people with a handshake, though it is very popular among foreigners, and say nothing of embracing or kissing when greeting or saying good-bye. Consequently, it is better not to behave too carefree in public, even though you are well-intentioned. Also, it is advisable to be fairly cautious in political discussions. Do not particularly push yourself forward, or else you are unwelcome.

To sum up, do in Rome as Rome does, but you need not worry about these cultural barriers since most Chinese are hospitable and friendly and will not mind your no accomplishment.

小题1:In most Chinese’s eyes, the fundamental glue holding society together is the idea of ____.

A.relationships between people

B.influences upon others

C.dependence on others

D.kindness to others小题2:The underlined word “demean” in the first paragraph means make people _____.

A.respectful

B.happy

C.shameful

D.weak小题3:Which of the following is NOT mentioned in the passage?

A.It is impolite to insult, embarrass, shame or shout at a person.

B.It is polite that you should bring gifts to others when invited to dinner.

C.It is necessary to show your character of being considerate, polite, and well mannered.

D.It is important for the Chinese to have good relationships between people.小题4: Which of the following proverbs has the same meaning as the underlined sentence “Do in Rome as Rome does.”?

A.Caution is the parent of safety.

B.Many hands make light work.

C.There’s no smoke without fire.

D.If you are elsewhere, live as they do there.